Pulmonary Artery Aneurysm-Related Fatal Hemoptysis in Behcet's Disease: A Case Report with Literature Review
Abstract
Introduction
Behcet's disease is a multisystemic disorder of unknown etiology. Vascular involvement is identified by the development of aneurysms and occlusion of the vessels. The current report aimed to discuss a case of Behcet disease presented with a bilateral pulmonary aneurysm.
Case presentation
A 41-year-old woman presented with recurrent attacks of hemoptysis for two years. A chest computed tomography scan revealed bilateral pulmonary artery aneurysm. Repeated bronchoscopy showed bleeding from the right lower lobe bronchus. She underwent a right-side thoracotomy with a right lower lobectomy. She was scheduled for left-side intervention as well. Before discharge, she was seen by a rheumatologist and was diagnosed with a case of Behcet disease. She developed attacks of massive hemoptysis (huge and bright blood) after two weeks which led to her passing away.
Conclusion
Although it is rare, Behcet disease could involve major arteries and lead to fatal complications. Surgical intervention remained a viable option for the management.
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